Drugs / Ataluren

Regulatory milestones approvals, filings & regulatory actions · 2 recorded

MilestoneJurisdictionBrandIndicationDateSentence it was read from
Withdrawn EU (EMA) Translarna 2025-03-28 europa.eu
Approved · conditional EU (EMA) Translarna 2014-07-31 europa.eu

Trials 31 · a red edge is where a trial was stopped

PhaseRegistry idDatesIndicationSponsorStatusOutcome
Phase 11 trial
Phase 1 NCT02409004 Feb → Mar 2015 PTC Therapeutics Completed No outcome recorded
Phase 1/21 trial
Phase 1/2 NCT04014530 Aug 2019 → Jun 2023 overdue colorectal cancer, endometrial cancer Academic Medical Center - University of Amsterdam Recruiting No outcome recorded
Phase 217 trials
Phase 2 NCT04336826 Dec 2021 → Aug 2023 Duchenne muscular dystrophy PTC Therapeutics Completed No outcome recorded
Phase 2 NCT03796637 Apr → Jun 2019 Duchenne muscular dystrophy PTC Therapeutics Completed No outcome recorded
Phase 2 NCT04117880 Dec 2018 → Jan 2021 aniridia PTC Therapeutics Withdrawn No outcome recorded
Phase 2 NCT03648827 Dec 2018 → Oct 2020 Duchenne muscular dystrophy PTC Therapeutics Completed No outcome recorded
Phase 2 NCT02819557 Jun 2016 → Feb 2018 Duchenne muscular dystrophy PTC Therapeutics Completed No outcome recorded
Phase 2 NCT02647359 Jan 2016 → Jan 2021 aniridia PTC Therapeutics Completed No outcome recorded
Phase 2 NCT01141075 Jul 2010 → Nov 2011 inborn disorder of amino acid metabolism PTC Therapeutics Terminated No outcome recorded
Phase 2 NCT01009294 Jan → Mar 2010 Becker muscular dystrophy, Duchenne muscular dystrophy PTC Therapeutics Terminated No outcome recorded
Phase 2 NCT00947193 Oct 2009 → Aug 2011 hemophilia A, hemophilia B PTC Therapeutics Terminated No outcome recorded
Phase 2 NCT00847379 Jan 2009 → May 2010 Becker muscular dystrophy, Duchenne muscular dystrophy PTC Therapeutics Terminated No outcome recorded
Phase 310 trials
Phase 3 NCT03179631 Jul 2017 → Mar 2022 Duchenne muscular dystrophy, X-linked disease, atrophic muscular disease PTC Therapeutics Completed No outcome recorded
Phase 3 NCT02456103 Aug 2015 → Jun 2017 cystic fibrosis PTC Therapeutics Terminated No outcome recorded
Phase 3 NCT02139306 Aug 2014 → Nov 2016 cystic fibrosis PTC Therapeutics Completed No outcome recorded
Phase 3 NCT02107859 May 2014 → Jun 2017 cystic fibrosis PTC Therapeutics Terminated No outcome recorded
Phase 3 NCT02090959 Mar 2014 → Jun 2018 Duchenne muscular dystrophy, X-linked disease, atrophic muscular disease PTC Therapeutics Terminated No outcome recorded
Phase 3 NCT01826487 Mar 2013 → Aug 2015 Duchenne muscular dystrophy, X-linked disease, atrophic muscular disease PTC Therapeutics Completed No outcome recorded
Phase 3 NCT01557400 May 2012 → Jan 2018 Becker muscular dystrophy, Duchenne muscular dystrophy, neuromuscular disease caused by qualitative or quantitative defects of dystrophin PTC Therapeutics Completed No outcome recorded
Phase 3 NCT01247207 Nov 2010 → Feb 2026 Duchenne muscular dystrophy PTC Therapeutics Completed No outcome recorded
Phase 3 NCT01140451 Aug 2010 → Dec 2013 cystic fibrosis PTC Therapeutics Completed No outcome recorded
Phase 3 NCT00803205 Sep 2009 → Nov 2011 cystic fibrosis PTC Therapeutics Completed No outcome recorded
Phase 42 trials
Phase 4 NCT03256799 Mar → Jul 2017 cystic fibrosis University of Alabama at Birmingham Completed No outcome recorded
Phase 4 NCT03256968 Jan 2017 → Dec 2018 cystic fibrosis University of Alabama at Birmingham Completed No outcome recorded
Also used as a comparator or background therapy in 1 trial
PhaseRegistry idDatesIndicationSponsorStatusOutcome
Phase 2 NCT02758626 Comparator Nov 2016 → Feb 2021 epilepsy NYU Langone Health Completed No outcome recorded

Evidence & citations 9 cited values

Every value below carries the sentence it was read from. 35 sources stand behind the page.

FieldValueCited text
Known as ataluren Ataluren (PTC124) enables ribosomal readthrough of premature stop codons, leading to production of full-length, functional proteins.” PMID 24349052 Dec 2013
30

“Chronic ataluren (PTC124) treatment of nonsense mutation cystic fibrosis.” PMID 21233271 Jan 2011

NCT00237380

NCT04117880

NCT02647359

NCT00759876

NCT02107859

NCT02456103

NCT02090959

NCT03179631

NCT02139306

NCT03256799

NCT01247207

NCT01009294

NCT01826487

NCT01557400

NCT02819557

NCT03256968

NCT02409004

NCT00592553

NCT01141075

NCT02758626

NCT01140451

NCT00947193

NCT00458341

NCT00803205

NCT00847379

NCT03648827

NCT03796637

NCT04336826

NCT04014530

Known as Ataluren(PTC124) Ataluren(PTC124)NCT02409004
Known as Atalureno ChEMBL registry synonym — accepted as the source's own label CHEMBL256997
Known as PTC124 “Ataluren (PTC124) enables ribosomal readthrough of premature stop codons, leading to production of full-length, functional proteins.” PMID 24349052 Dec 2013
7

“Long-Term Treatment With Ivacaftor in Combination With Ataluren (PTC124) in Subjects With Nonsense Mutation Cystic Fibrosis” NCT03256968

“Phase 2a Extension Study of Ataluren (PTC124) in Duchenne Muscular Dystrophy (DMD)” NCT00759876

“Drug: Ataluren (PTC124®)” NCT02139306

“Ataluren (PTC124)” NCT03256799

PTC124NCT04117880

NCT00351078

NCT00234663

Known as Translarna ChEMBL registry synonym — accepted as the source's own label CHEMBL256997
Action Restore “PTC124 has been shown to partially restore CFTR production in animals with CF due to a nonsense mutation.” NCT00234663
Modality Small molecule “a 284-Dalton 1,2,4-oxadiazole” PMID 17389552 Apr 2007
Route Oral “A Phase 2 Study of PTC124 as an Oral Treatment for Nonsense-Mutation-Mediated Cystic Fibrosis” NCT00234663
Target CFTR “PTC124 has been shown to partially restore CFTR production in animals with CF due to a nonsense mutation.” NCT00234663